Rare Lung Diseases I – Lymphangioleiomyomatosis
نویسندگان
چکیده
منابع مشابه
Pulmonary lymphangioleiomyomatosis: a rare case.
Lymphangioleiomyomatosis is an uncommon lung disease primarily affecting women of childbearing age. It is characterized by the progressive proliferation and infiltration of smooth muscle-like cells, which lead to cystic destruction of the lung parenchyma; obstruction of airways, blood vessels, and lymphatics; and loss of pulmonary function. We present the case of a 46-year-old female patient wi...
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Background: Lymphangioleiomyomatosis (LAM) is a progressive lungs disease that affects women at reproductive years. Sirolimus inhibits mammalian target of rapamycin (mTOR) and its administration in past studies was hopeful in treatment of patients with LAM. The aim of this study was to evaluate sirolimus therapy on lung function in LAM patients. Methods: We conducted a trial to evaluate the ef...
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General Practitioners need support to recognise rare lung disorders and advise patients on the best available care http://ow.ly/kDgy304rX94.
متن کاملLiving-donor lobar lung transplantation for lymphangioleiomyomatosis.
Living-donor lobar lung transplantation seems to be best suited for children and small adults because only two lobes are transplanted. However, the amount of tolerable size discrepancy between donors and recipients is currently unknown. We report two cases of lymphangioleiomyomatosis with hyperinflation successfully treated with living-donor lobar lung transplantation in spite of large size dis...
متن کاملLung Transplantation for Lymphangioleiomyomatosis in Japan
BACKGROUND Lung transplantation has been established as the definitive treatment option for patients with advanced lymphangioleiomyomatosis (LAM). However, the prognosis after registration and the circumstances of lung transplantation with sirolimus therapy have never been reported. METHODS In this national survey, we analyzed data from 98 LAM patients registered for lung transplantation in t...
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ژورنال
عنوان ژورنال: Canadian Respiratory Journal
سال: 2006
ISSN: 1198-2241
DOI: 10.1155/2006/696573